Found 1969 results
Bargiela D & Chinnery PF (2017) Mitochondria in neuroinflammation - Multiple sclerosis (MS), leber hereditary optic neuropathy (LHON) and LHON-MS. Neurosci Lett
Prudent J & McBride HM (2017) The mitochondria-endoplasmic reticulum contact sites: a signalling platform for cell death. Curr Opin Cell Biol 47, 52-63
Dehez F, Schanda P, King MS, Kunji ERS & Chipot C (2017) Mitochondrial ADP/ATP Carrier in Dodecylphosphocholine Binds Cardiolipins with Non-native Affinity. Biophys J 113, 2311-2315
Fernandez-Vizarra E & Zeviani M (2017) Mitochondrial complex III Rieske Fe-S protein processing and assembly. Cell Cycle, 1-25
Widdrington JD, Gomez-Duran A, Steyn JS, Pyle A, Ruchaud-Sparagano M-H, Scott J, Baudouin SV, Rostron AJ, Simpson J & FMedSci PFChinnery (2017) Mitochondrial DNA depletion induces innate immune dysfunction rescued by interferon-γ. J Allergy Clin Immunol
Wei W, Keogh MJ, Wilson I, Coxhead J, Ryan S, Rollinson S, Griffin H, Kurzawa-Akanbi M, Santibanez-Koref M, Talbot K, Turner MR, McKenzie C-A, Troakes C, Attems J, Smith C, Sarraj SAl, Morris CM, Ansorge O, Pickering-Brown S, Ironside JW & Chinnery PF (2017) Mitochondrial DNA point mutations and relative copy number in 1363 disease and control human brains. Acta Neuropathol Commun 5, 13
Gammage PA, Moraes CT & Minczuk MA (2017) Mitochondrial Genome Engineering: The Revolution May Not Be CRISPR-Ized. Trends Genet
Nesci S (2017) Mitochondrial permeability transition, F1FO-ATPase and calcium: an enigmatic triangle. EMBO Rep
Yu EPK, Reinhold J, Yu H, Starks L, Uryga AK, Foote K, Finigan A, Figg N, Pung Y-F, Logan A, Murphy MP & Bennett M (2017) Mitochondrial Respiration Is Reduced in Atherosclerosis, Promoting Necrotic Core Formation and Reducing Relative Fibrous Cap Thickness. Arterioscler Thromb Vasc Biol 37, 2322-2332
Formentini L, Santacatterina F, de Arenas CNúñez, Stamatakis K, López-Martínez D, Logan A, Fresno M, Smits R, Murphy MP & Cuezva JM (2017) Mitochondrial ROS Production Protects the Intestine from Inflammation through Functional M2 Macrophage Polarization. Cell Rep 19, 1202-1213
Liu X, Murphy MP, Xing W, Wu H, Zhang R & Sun H (2017) Mitochondria-targeted antioxidant MitoQ reduced renal damage caused by ischemia-reperfusion injury in rodent kidneys: Longitudinal observations of T2 -weighted imaging and dynamic contrast-enhanced MRI. Magn Reson Med
Vilaseca M, García-Calderó H, Lafoz E, Ruart M, López-Sanjurjo CIsabel, Murphy MP, Deulofeu R, Bosch J, Hernández-Gea V, Gracia-Sancho J & García-Pagán JCarlos (2017) Mitochondria-targeted antioxidant mitoquinone deactivates human and rat hepatic stellate cells and reduces portal hypertension in cirrhotic rats. Liver Int
Smith AC, Eyassu F, Mazat J-P & Robinson AJ (2017) MitoCore: a curated constraint-based model for simulating human central metabolism. BMC Syst Biol 11, 114
Shchepinova MM, Cairns AG, Prime TA, Logan A, James AM, Hall AR, Vidoni S, Arndt S, Caldwell ST, Prag HA, Pell VR, Krieg T, Mulvey JF, Yadav P, Cobley JN, Bright TP, Senn HM, Anderson RF, Murphy MP & Hartley RC (2017) MitoNeoD: A Mitochondria-Targeted Superoxide Probe. Cell Chem Biol
Springett R, King MS, Crichton PG & Kunji ERS (2017) Modelling the free energy profile of the mitochondrial ADP/ATP carrier. Biochim Biophys Acta 1858, 906-914
Crichton PG, Lee Y & Kunji ERS (2017) The molecular features of uncoupling protein 1 support a conventional mitochondrial carrier-like mechanism. Biochimie 134, 35-50
Steele HE, Horvath R, Lyon JJ & Chinnery PF (2017) Monitoring clinical progression with mitochondrial disease biomarkers. Brain 140, 2530-2540
Vidoni S, Harbour ME, Guerrero-Castillo S, Signes A, Ding S, Fearnley IM, Taylor RW, Tiranti V, Arnold S, Fernandez-Vizarra E & Zeviani M (2017) MR-1S Interacts with PET100 and PET117 in Module-Based Assembly of Human Cytochrome c Oxidase. Cell Rep 18, 1727-1738
Viscomi C & Zeviani M (2017) MtDNA-maintenance defects: syndromes and genes. J Inherit Metab Dis
Morita M, Prudent J, Basu K, Goyon V, Katsumura S, Hulea L, Pearl D, Siddiqui N, Strack S, McGuirk S, St-Pierre J, Larsson O, Topisirovic I, Vali H, McBride HM, Bergeron JJ & Sonenberg N (2017) mTOR Controls Mitochondrial Dynamics and Cell Survival via MTFP1. Mol Cell 67, 922-935.e5
Keogh MJ, Jaiser SR, Steele HE, Horvath R, Chinnery PF & Baker MR (2017) mutations and central demyelination: Evidence from electrophysiologic phenotyping in female manifesting carriers. Neurol Clin Pract 7, 451-454
Connor TM, Hoer S, Mallett A, Gale DP, Gomez-Duran A, Posse V, Antrobus R, Moreno P, Sciacovelli M, Frezza C, Duff J, Sheerin NS, Sayer JA, Ashcroft M, Wiesener MS, Hudson G, Gustafsson CM, Chinnery PF & Maxwell PH (2017) Mutations in mitochondrial DNA causing tubulointerstitial kidney disease. PLoS Genet 13, e1006620
Kasapkara ÇSeher, Tümer L, Zanetti N, Ezgü F, Lamantea E & Zeviani M (2017) A Myopathy, Lactic Acidosis, Sideroblastic Anemia (MLASA) Case Due to a Novel PUS1 Mutation. Turk J Haematol 34, 376-377
Flønes IH, Fernandez-Vizarra E, Lykouri M, Brakedal B, Skeie GOlve, Miletic H, Lilleng PK, Alves G, Tysnes O-B, Haugarvoll K, Dölle C, Zeviani M & Tzoulis C (2017) Neuronal complex I deficiency occurs throughout the Parkinson's disease brain, but is not associated with neurodegeneration or mitochondrial DNA damage. Acta Neuropathol
Vantroys E, Larson A, Friederich M, Knight K, Swanson MA, Powell CA, Smet J, Vergult S, De Paepe B, Seneca S, Roeyers H, Menten B, Minczuk MA, Vanlander A, Van Hove J & Van Coster R (2017) New insights into the phenotype of FARS2 deficiency. Mol Genet Metab