Found 1937 results
Jurkute N, Leu C, Pogoda H-M, Arno G, Robson AG, Nürnberg G, Altmüller J, Thiele H, Motameny S, Toliat MReza, Powell K, Höhne W, Michaelides M, Webster AR, Moore AT, Hammerschmidt M, Nürnberg P, Yu-Wai-Man P & Votruba M (2019) SSBP1 mutations in dominant optic atrophy with variable retinal degeneration. Ann Neurol
Ruprecht JJ & Kunji ERs (2019) Structural changes in the transport cycle of the mitochondrial ADP/ATP carrier. Curr Opin Struct Biol 57, 135-144
Guo H, Suzuki T & Rubinstein JL (2019) Structure of a bacterial ATP synthase. Elife 8
Petri J, Nakatani Y, Montgomery MG, Ferguson SA, Aragão D, Leslie AGW, Heikal A, Walker JE & Cook GM (2019) Structure of F-ATPase from the obligate anaerobe Fusobacterium nucleatum. Open Biol 9, 190066
Park J, Lee S-Y, Jeong H, Kang M-G, Van Haute L, Minczuk M, Seo JKon, Jun Y, Myung K, Rhee H-W & Lee C (2019) The structure of human EXD2 reveals a chimeric 3' to 5' exonuclease domain that discriminates substrates via metal coordination. Nucleic Acids Res 47, 7078-7093
Zhang AT, Montgomery MG, Leslie AGW, Cook GM & Walker JE (2019) The structure of the catalytic domain of the ATP synthase from is a target for developing antitubercular drugs. Proc Natl Acad Sci U S A
Kim Y-R, Baek J-I, Kim SHwan, Kim M-A, Lee B, Ryu N, Kim K-H, Choi D-G, Kim H-M, Murphy MP, Macpherson G, Choo Y-S, Bok J, Lee K-Y, Park J-W & Kim U-K (2019) Therapeutic potential of the mitochondria-targeted antioxidant MitoQ in mitochondrial-ROS induced sensorineural hearing loss caused by Idh2 deficiency. Redox Biol 20, 544-555
Jurkute N, Harvey J & Yu-Wai-Man P (2019) Treatment strategies for Leber hereditary optic neuropathy. Curr Opin Neurol 32, 99-104
Tavoulari S, Thangaratnarajah C, Mavridou V, Harbour ME, Martinou J-C & Kunji ERs (2019) The yeast mitochondrial pyruvate carrier is a hetero-dimer in its functional state. EMBO J 38
Mills EL, Pierce KA, Jedrychowski MP, Garrity R, Winther S, Vidoni S, Yoneshiro T, Spinelli JB, Lu GZ, Kazak L, Banks AS, Haigis MC, Kajimura S, Murphy MP, Gygi SP, Clish CB & Chouchani ET (2018) Accumulation of succinate controls activation of adipose tissue thermogenesis. Nature 560, 102-106
Ferguson DCJ, Smerdon GR, Harries LW, Dodd NJF, Murphy MP, Curnow A & Winyard PG (2018) Altered cellular redox homeostasis and redox responses under standard oxygen cell culture conditions versus physioxia. Free Radic Biol Med 126, 322-333
Signes A & Fernandez-Vizarra E (2018) Assembly of mammalian oxidative phosphorylation complexes I-V and supercomplexes. Essays Biochem 62, 255-270
He J, Ford HC, Carroll J, Douglas C, Gonzales E, Ding S, Fearnley IM & Walker JE (2018) Assembly of the membrane domain of ATP synthase in human mitochondria. Proc Natl Acad Sci U S A
Montgomery MG, Gahura O, Leslie AGW, Zíková A & Walker JE (2018) ATP synthase fromhas an elaborated canonical F-domain and conventional catalytic sites. Proc Natl Acad Sci U S A 115, 2102-2107
Kim M, Stepanova A, Niatsetskaya Z, Sosunov S, Arndt S, Murphy MP, Galkin A & Ten VS (2018) Attenuation of oxidative damage by targeting mitochondrial complex I in neonatal hypoxic-ischemic brain injury. Free Radic Biol Med 124, 517-524
Lee JJ, Sanchez-Martinez A, Zarate AMartinez, Benincá C, Mayor U, Clague MJ & Whitworth AJ (2018) Basal mitophagy is widespread inbut minimally affected by loss of Pink1 or parkin. J Cell Biol
Harborne SPD & Kunji ERS (2018) Calcium-regulated mitochondrial ATP-Mg/P carriers evolved from a fusion of an EF-hand regulatory domain with a mitochondrial ADP/ATP carrier-like domain. IUBMB Life 70, 1222-1232
Duncan AL, Ruprecht JJ, Kunji ERS & Robinson AJ (2018) Cardiolipin dynamics and binding to conserved residues in the mitochondrial ADP/ATP carrier. Biochim Biophys Acta 1860, 1035-1045
Keogh MJ, Steele HE & Chinnery PF (2018) Cardiovascular Genetics and GenomicsMitochondrial Cardiovascular Diseases (Kumar D, and Elliott Peds.), Springer International Publishing, Cham
James AM, Smith CL, Smith AC, Robinson AJ, Hoogewijs K & Murphy MP (2018) The Causes and Consequences of Nonenzymatic Protein Acylation. Trends Biochem Sci
Sharma S, Singh P, Fernandez-Vizarra E, Zeviani M, van der Knaap MS & Saran RKumar (2018) Cavitating Leukoencephalopathy With Posterior Predominance Caused by a Deletion in the APOPT1 Gene in an Indian Boy. J Child Neurol 33, 428-431
Walker JE (2018) in Mechanisms of Primary Energy Transduction in Biology Mechanisms of Primary Energy Transduction in Biology pp. 338-373, The Royal Society of Chemistry
Lovero D, Giordano L, Marsano RMassimilia, Sanchez-Martinez A, Boukhatmi H, Drechsler M, Oliva M, Whitworth AJ, Porcelli D & Caggese C (2018) Characterization of Drosophila ATPsynC mutants as a new model of mitochondrial ATP synthase disorders. PLoS One 13, e0201811
Rossman MJ, Santos-Parker JR, Steward CAC, Bispham NZ, Cuevas LM, Rosenberg HL, Woodward KA, Chonchol M, Gioscia-Ryan RA, Murphy MP & Seals DR (2018) Chronic Supplementation With a Mitochondrial Antioxidant (MitoQ) Improves Vascular Function in Healthy Older Adults. Hypertension
Repp BM, Mastantuono E, Alston CL, Schiff M, Haack TB, Rötig A, Ardissone A, Lombes A, Catarino CB, Diodato D, Schottmann G, Poulton J, Burlina A, Jonckheere A, Munnich A, Rolinski B, Ghezzi D, Rokicki D, Wellesley D, Martinelli D, Wenhong D, Lamantea E, Ostergaard E, Pronicka E, Pierre G, Smeets HJM, Wittig I, Scurr I, de Coo IFM, Moroni I, Smet J, Mayr JA, Dai L, De Meirleir L, Schuelke M, Zeviani M, Morscher RJ, McFarland R, Seneca S, Klopstock T, Meitinger T, Wieland T, Strom TM, Herberg U, Ahting U, Sperl W, Nassogne M-C, Ling H, Fang F, Freisinger P, Van Coster R, Strecker V, Taylor RW, Häberle J, Vockley J, Prokisch H & Wortmann S (2018) Clinical, biochemical and genetic spectrum of 70 patients with ACAD9 deficiency: is riboflavin supplementation effective?. Orphanet J Rare Dis 13, 120