Found 2065 results
Szibor M, Gainutdinov T, Fernandez-Vizarra E, Dufour E, Gizatullina Z, Debska-Vielhaber G, Heidler J, Wittig I, Viscomi C, Gellerich F & Moore AL (2019) Bioenergetic consequences from xenotopic expression of a tunicate AOX in mouse mitochondria: Switch from RET and ROS to FET. Biochim Biophys Acta Bioenerg, 148137
Viscomi C & Zeviani M (2019) Breathe: Your Mitochondria Will Do the Rest… If They Are Healthy!. Cell Metabolism 30, 628 - 629
Hirst J, Kunji ERS & Walker JE (2019) Comment on "Protein assemblies ejected directly from native membranes yield complexes for mass spectrometry". Science 366
Tufi R, Gleeson TP, von Stockum S, Hewitt VL, Lee JJ, Terriente-Felix A, Sanchez-Martinez A, Ziviani E & Whitworth AJ (2019) Comprehensive Genetic Characterization of Mitochondrial Ca Uniporter Components Reveals Their Different Physiological Requirements In Vivo. Cell Rep 27, 1541-1550. e1545
Boczonadi V, King MS, Smith AC, Olahova M, Bansagi B, Roos A, Eyassu F, Borchers C, Ramesh V, Lochmüller H, Polvikoski T, Whittaker RG, Pyle A, Griffin H, Taylor RW, Chinnery PF, Robinson AJ, Kunji ERS & Horvath R (2019) Correction: Mitochondrial oxodicarboxylate carrier deficiency is associated with mitochondrial DNA depletion and spinal muscular atrophy-like disease. Genet Med
Kohlhauer M, Pell VR, Burger N, Spiroski AM, Gruszczyk A, Mulvey JF, Mottahedin A, Costa ASH, Frezza C, Ghaleh B, Murphy MP, Tissier R & Krieg T (2019) Correction to: Protection against cardiac ischemia-reperfusion injury by hypothermia and by inhibition of succinate accumulation and oxidation is additive. Basic Res Cardiol 114, 24
Ryan DG, Murphy MP, Frezza C, Prag HA, Chouchani ET, O'Neill LA & Mills EL (2019) Coupling Krebs cycle metabolites to signalling in immunity and cancer. Nat Metab 1, 16-33
Sobti M, Ishmukhametov R, Bouwer JC, Ayer A, Suarna C, Smith NJ, Christie M, Stocker R, Duncan TM & Stewart AG (2019) Cryo-EM reveals distinct conformations of ATP synthase on exposure to ATP. Elife 8
Gu J, Zhang L, Zong S, Guo R, Liu T, Yi J, Wang P, Zhuo W & Yang M (2019) Cryo-EM structure of the mammalian ATP synthase tetramer bound with inhibitory protein IF1. Science 364, 1068-1075
Chinnery PF & Prudent J (2019) De-fusing mitochondria defuses the mtDNA time-bomb. Cell Res
Domínguez-González C, Madruga-Garrido M, Mavillard F, Garone C, Aguirre-Rodríguez FJavier, M Donati A, Kleinsteuber K, Martí I, Martín-Hernández E, Morealejo-Aycinena JP, Munell F, Nascimento A, Kalko SG, M Sardina D, Del Vayo CÁlvarez, Serrano O, Long Y, Tu Y, Levin B, Thompson JLP, Engelstad K, Uddin J, Torres-Torronteras J, Jimenez-Mallebrera C, Martí R, Paradas C & Hirano M (2019) Deoxynucleoside Therapy for Thymidine Kinase 2-Deficient Myopathy. Ann Neurol
Lau GY, Barts N, Hartley RC, Tobler M, Richards JG, Murphy MP & Arndt S (2019) Detection of changes in mitochondrial hydrogen sulfide in the fish model (Poeciliidae). Biol Open 8
Parikh S, Karaa A, Goldstein A, Bertini ESilvio, Chinnery PF, Christodoulou J, Cohen BH, Davis RL, Falk MJ, Fratter C, Horvath R, Koenig MKay, Mancuso M, McCormack S, McCormick EM, McFarland R, Nesbitt V, Schiff M, Steele H, Stockler S, Sue C, Tarnopolsky M, Thorburn DR, Vockley J & Rahman S (2019) Diagnosis of 'possible' mitochondrial disease: an existential crisis. J Med Genet 56, 123-130
Ruprecht J & Kunji ERS (2019) Editorial overview: COSB Membranes. Curr Opin Struct Biol 57, vi-viii
Noli L, Khorsandi SE, Pyle A, Giritharan G, Fogarty N, Capalbo A, Devito L, Jovanovic VM, Khurana P, Rosa H, Kolundzic N, Cvoro A, Niakan KK, Malik A, Foulk R, Heaton N, Ardawi MSaleh, Chinnery PF, Ogilvie C, Khalaf Y & Ilic D (2019) Effects of Thyroid Hormone on Mitochondria and Metabolism of Human Preimplantation Embryos. Stem Cells
Hoitzing H, Gammage PA, Van Haute L, Minczuk M, Johnston IG & Jones NS (2019) Energetic costs of cellular and therapeutic control of stochastic mitochondrial DNA populations. PLoS Comput Biol 15, e1007023
Aloia L, McKie MAlexander, Vernaz G, Cordero-Espinoza L, Aleksieva N, van den Ameele J, Antonica F, Font-Cunill B, Raven A, Cigliano RAiese, Belenguer G, Mort RL, Brand AH, Zernicka-Goetz M, Forbes SJ, Miska EA & Huch M (2019) Epigenetic remodelling licences adult cholangiocytes for organoid formation and liver regeneration. Nature Cell Biology 21, 1321 - 1333
Nieminuszczy J, Broderick R, Bellani MA, Smethurst E, Schwab RA, Cherdyntseva V, Evmorfopoulou T, Lin Y-L, Minczuk M, Pasero P, Gagos S, Seidman MM & Niedzwiedz W (2019) EXD2 Protects Stressed Replication Forks and Is Required for Cell Viability in the Absence of BRCA1/2. Mol Cell
Boreikaite V, Wicky BIM, Watt IN, Clarke J & Walker JE (2019) Extrinsic conditions influence the self-association and structure of IF, the regulatory protein of mitochondrial ATP synthase. Proc Natl Acad Sci U S A 116, 10354-10359
Guyatt AL, Brennan RR, Burrows K, Guthrie PAI, Ascione R, Ring SM, Gaunt TR, Pyle A, Cordell HJ, Lawlor DA, Chinnery PF, Hudson G & Rodriguez S (2019) A genome-wide association study of mitochondrial DNA copy number in two population-based cohorts. Hum Genomics 13, 6
Wei W, Tuna S, Keogh MJ, Smith KR, Aitman TJ, Beales PL, Bennett DL, Gale DP, Bitner-Glindzicz MAK, Black GC, Brennan P, Elliott P, Flinter FA, R Floto A, Houlden H, Irving M, Koziell A, Maher ER, Markus HS, Morrell NW, Newman WG, Roberts I, Sayer JA, Smith KGC, Taylor JC, Watkins H, Webster AR, Wilkie AOM, Williamson C, Ashford S, Penkett CJ, Stirrups KE, Rendon A, Ouwehand WH, Bradley JR, F Raymond L, Caulfield M, Turro E & Chinnery PF (2019) Germline selection shapes human mitochondrial DNA diversity. Science 364
McGrath TM, Spreckley E, Rodriguez AFernandez, Viscomi C, Alamshah A, Akalestou E, Murphy KG & Jones NS (2019) The homeostatic dynamics of feeding behaviour identify novel mechanisms of anorectic agents. PLoS Biol 17, e3000482
Sommerville EW, Rosa IDalla, Rosenberg MM, Bruni F, Thompson K, Rocha M, Blakely EL, He L, Falkous G, Schaefer AM, Yu-Wai-Man P, Chinnery PF, Hedstrom L, Spinazzola A, Taylor RW & Gorman GS (2019) Identification of a novel heterozygous guanosine monophosphate reductase (GMPR) variant in a patient with a late-onset disorder of mitochondrial DNA maintenance. Clin Genet
Gómez-Cabañas L, López-Cotarelo P, Criado-García O, Murphy MP, Boya P & Rodríguez-Fernández JLuis (2019) Immunological Synapse Formation Induces Mitochondrial Clustering and Mitophagy in Dendritic Cells. The Journal of Immunology 202, 1715 - 1723
Costa R, Peruzzo R, Bachmann M, Montà GDalla, Vicario M, Santinon G, Mattarei A, Moro E, Quintana-Cabrera R, Scorrano L, Zeviani M, Vallese F, Zoratti M, Paradisi C, Argenton F, Brini M, Calì T, Dupont S, Szabó I & Leanza L (2019) Impaired Mitochondrial ATP Production Downregulates Wnt Signaling via ER Stress Induction. Cell Rep 28, 1949-1960.e6